NEUROFIBROMA PLEXIFORME MEDIASTINAL INFANTIL: UM ACHADO INCIDENTAL
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Keywords

Plexiform Neurofibroma
Mediastinum
Child

How to Cite

Vieira Donzelli, R., Alves Coelho Neto, M., Ramos dos Santos, M., Mathiazi Di Mateos, L., Favarin da Silva, E., Lorraine de Sousa Oliveira, E., Girelli Neto, S., Kuranishi, M. E., Gruber Colombo, M., José Paludo Petek, D., Gonçalves Dos Santos Ody, G., Porfirio da Silva Neto, F., Stefaniak, L., Maria Lima Aguiar Mundim, O., & Geraldo Coelho Júnior, L. (2024). NEUROFIBROMA PLEXIFORME MEDIASTINAL INFANTIL: UM ACHADO INCIDENTAL. Brazilian Journal of Implantology and Health Sciences, 6(12), 53–62. https://doi.org/10.36557/2674-8169.2024v6n12p53-62

Abstract

Introduction: This case report addresses plexiform neurofibroma, a rare benign tumor that originates in the sheaths of peripheral nerves and which, although more common in superficial regions, can occur in deep areas such as the mediastinum, presenting diagnostic and therapeutic challenges. Methodology: Data collection was carried out through a detailed analysis of the patient's medical records, with information about the clinical history, imaging exams and surgical procedure, in addition to interviews with legal guardians. Case description: 7-year-old patient, incidentally diagnosed with mediastinal plexiform neurofibroma during a computed tomography scan performed to investigate flu-like symptoms. The tumor was located in the posterior mediastinum, firmly attached to the thoracic aorta, and was removed by videothoracoscopy. Discussion: The location of neurofibroma in the mediastinum is uncommon and, despite being benign, the tumor presents surgical challenges due to its proximity to vital structures. The choice for a minimally invasive approach was appropriate and is in line with the literature on the management of mediastinal tumors. Conclusion: The case highlights the importance of early diagnosis and minimally invasive surgical treatment, in addition to the need for long-term follow-up, considering the risk of recurrence or malignant transformation.

https://doi.org/10.36557/2674-8169.2024v6n12p53-62
PDF (Português (Brasil))

References

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Creative Commons License

This work is licensed under a Creative Commons Attribution 4.0 International License.

Copyright (c) 2024 Renato Vieira Donzelli, Murilo Alves Coelho Neto, Mateus Ramos dos Santos, Lívia Mathiazi Di Mateos, Emilly Favarin da Silva, Evellyn Lorraine de Sousa Oliveira, Saul Girelli Neto, Maria Eduarda Kuranishi, Mateus Gruber Colombo, Dionísio José Paludo Petek, Gabriel Gonçalves Dos Santos Ody, Francisco Porfirio da Silva Neto, Luciano Stefaniak, Olga Maria Lima Aguiar Mundim, Luilson Geraldo Coelho Júnior

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